Summary
Juxta-articular adiposis dolorosa is a rare subtype of Dercum’s disease. It manifests mainly on the medial parts of the knees. Pain and impaired mobility are common symptoms. We report on four females (aged between 52 and 83 years) who suffered from juxta-articular adiposis dolorosa for more than 10 years. These patients were successfully treated by dermolipectomy resulting in dramatically improved pain and mobility. Adverse effects and complications were minor with a lymph fistula in a single patient which was treated by surgery.
Zusammenfassung
Die juxtaartikuläre Adiposis dolorosa ist ein seltener Subtyp des Mb. Dercum. Er manifestiert sich hauptsächlich am medialen Knie. Schmerzen und Bewegungsbehinderungen sind häufige Symptome. Wir berichten über 4 Frauen (Alter zwischen 52 und 83 Jahren), die an einer juxtaartikulären Adiposis dolora über mehr als 10 Jahren litten. Die Patienten wurden erfolgreich mittels Dermolipektomie behandelt, was sich in einer dramatischen Verbesserung von Schmerzen und Mobilität zeigte. Komplikationen waren geringgradig. Bei einer Patientin kam es temporär zu einer Lymphfistel, die chirurgisch behandelt wurde.
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U. Wollina, B. Heinig, D. Langner, and A. Nowak delcare that there are no actual or potential conflicts of interest in relation to this article.
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Wollina, U., Heinig, B., Langner, D. et al. Juxta-articular adiposis dolorosa (Dercum’s disease type IV): report of four cases and treatment by dermolipectomy. Wien Med Wochenschr 165, 374–377 (2015). https://doi.org/10.1007/s10354-015-0378-1
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DOI: https://doi.org/10.1007/s10354-015-0378-1